Clinical, Audiological and Radiological Features of Bilateral Enlarged Vestibular Aqueducts Syndrome: Case Series

DOI

10.2991/978-94-6463-280-4_27How to use a DOI?

Keywords

Enlarge Vestibular Aqueducts (EVA); Hearing Loss; Hearing Aids

ABSTRACT

Background: Enlarge Vestibular Aqueducts (EVA) is a vestibular aqueduct dilation bigger than 1 mm which can cause progressive hearing loss. EVA diagnosis regards clinical features, audiological examination, CT Scan and/or MRI. Objectives: Describing the knowledge about clinical features, audiological and radiological examinations and management of 3 EVA patients. Case Report: Three patients were diagnosed with bilateral progressive hearing loss. The first patient, a 12-year-old boy with a chief complaint of decreased hearing in both ears since 3 years had PTA examination showing Severe MHL (86.25 dB) in the right ear and moderate MHL (55.75 dB) in the left ear. The CT scan showed 2.5 mm dilation in vestibular aqueduct of the right ear and 2.44 mm in the left ear. The second patient, a 12-year-old boy complained of having experienced progressive hearing loss in both ears for 7 years. PTA examination showed moderate Severe SNHL 65 dB in the right ear and 63.75 dB in the left ear and 2.8 mm enlarged aqueduct in the right ear and the left ear. The third patient, an 18-year-old woman had experienced hearing loss for 3 years. PTA examination resulted in moderate Severe SNHL 57.5 dB in the right ear and 56.25 dB in the left ear. The CT scan found aqueductal dilation of

1.5 mm in the right ear and 1.6 mm in the left ear. Three patients were given hearing aids and follow-up examination every 3 months to evaluate the hearing status, progression and effectiveness of hearing aids. hearing aids interventions were found quite effective in 2 patients, and it was regarded less optimal in 1 patient. The three patients were taught about the management of cochlear implants (CI) if hearing aids no longer effective. Methods: Relevant literatures were collected from Pubmed database using certain keywords and predetermined inclusion criteria. Results: Four articles relevant to this case series were obtained. Conclusion: EVA is a disorder of the inner ear that causes progressive sensorineural hearing loss. Correct diagnosis can be made based on careful analysis of the medical history, audiometric examination, CT scan and or MRI in order to determine appropriate management and anticipate progressive symptoms.

Copyright

© 2023 The Author(s)

Open Access

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TY  - CONF
AU  - Selvie Sira
AU  - Masyita Gaffar
AU  - Sri Wartati
PY  - 2023
DA  - 2023/10/31
TI  - Clinical, Audiological and Radiological Features of Bilateral Enlarged Vestibular Aqueducts Syndrome: Case Series
BT  - Proceedings of the 19 th Otorhinolaryngology head and neck surgery national congress (PERHATIKL 2022)
PB  - Atlantis Press
SP  - 150
EP  - 155
SN  - 2468-5739
UR  - https://doi.org/10.2991/978-94-6463-280-4_27
DO  - 10.2991/978-94-6463-280-4_27
ID  - Sira2023
ER  -